Классификация и клинические проявления гемифациальной микросомии (с обзором литературы)

Yakubov R.K., Yusupalieva K.B., Yakubov R.R., Abdukakharov A.K.

doi:10.57231/j.idmfs.2026.5.2.003

Classification and clinical manifestation of hemifacial microsomia (with a literature review)

Authors

Yakubov R.K., Yusupalieva K.B., Yakubov R.R., Abdukakharov A.K.

DOI:

https://doi.org/10.57231/j.idmfs.2026.5.2.003

Keywords:

Classification and clinical manifestation of hemifacial microsomia (with a literature review)

Abstract

Craniofacial microsomia (CFM) is the second most common congenital facial anomaly after cleft lip and palate. Based on a review of the literature, the authors present a chronological overview of the existing and most frequently used classification systems. The development of numerous classifications has primarily been associated with the pronounced polymorphism of clinical manifestations of hemifacial microsomia, as well as their application in surgical treatment planning and outcome assessment. According to the general consensus, the classifications presented above are not fully adequate for selecting optimal treatment strategies or for evaluating treatment outcomes. Analysis of the clinical material demonstrated the highest frequency of presentations with type I involvement - characterized by a hypoplastic temporomandibular joint - observed in 70 patients (60%). The majority of these patients were aged 13 -18 years (36 patients). with type IIa 20 patients -17.2%. With type IIb - 17 (14,6%), type III-9 patients (7.8%), type IV -3 patients (2,6%). For the determination of surgical treatment protocols, the Pruzansky classification, later modified by L. B. Kaban, is considered particularly informative..

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